Program Outline

For an explanation of "Laptop session" , Meet-the Expert session" and "Clinical Challenges for Diagnosis" look at the end of the program.

Thursday 2 September 2010

   

16.30

Opening ceremony

  Chairs: J.W.M. van der Meer, The Netherlands & A. Simon, The Netherlands
16.30 Opening
  J.W.M. van der Meer, The Netherlands
16.45 Deficiency of Interleukin-1 receptor antagonist (DIRA)
  I. Aksentijevich, USA
   
17.30 Art lecture
  Gary Schwartz, Art historian
   

19.00

Walking dinner

 

 

Friday 3 September 2010

   

08.00

Breakfast Meet-the-Expert session 1

  Clinical Phenotype of FMF
  A. Livneh, Israel & M. Tunca, Turkey
 

Breakfast Meet-the-Expert session 2

  Clinical Phenotype of HIDS
  J.W.M. van der Meer, The Netherlands & J. Frenkel, The Netherlands, A. Prieur, France
 

Breakfast Meet-the-Expert session 3

  Basic science Studying inflammasome
  S. Masters, Ireland & V. Hornung, Germany
   

09.00

Plenary session: FMF + PAPA

  Chairs: E. Ben-Chetrit, Israel & D. Kastner, USA
09.00 Environmental effects in FMF
  S. Özen, Turkey
09.30 Regulation of MEFV gene expression
  I. Touitou, France
10.00 The Effect of Colchicine on Pyrin-PSTPIP1 Interaction
  Z.E. Taskiran, Turkey
10.15 Peripheral blood mononuclear cell (PBMC) cultures of M694V homozygous FMF patients reveal a predisposition to secrete high levels of IL-17 given a T cell activation signal.
  Y. Shinar, Israel
   

10.30

Coffee break

   

11.00

Plenary session: Oral presentations FMF + PAPA

  Chairs: E. Ben-Chetrit, Israel & D. Kastner, USA
11.00

The effect of H. Pylori eradication in colchicine-resistant Familial Mediterranean Fever (FMF) Patients

  G. Hakobyan, Armenia
11.15 Validation of the newly developed pediatric criteria for the diagnosis of Familiar Mediterranean fever in a  large pediatric cohort of western European children with periodic fever
 

S. Federici, Italy

11.30 Is familial mediterranean fever (FMF) associated with non-alcoholic fatty liver disease(NAFLD)?
  M. Rozenbaum, Israel
11.45 Analysis of MEFV exon methylation  and expression patterns in familial mediterranean fever
  E.T. Turanli, Turkey
   
12.00 Lunch
   
12.00 Laptop presentations
   
13.00

Plenary session: Clinical challenges for diagnosis: plenary discussion with expert panel

  Chair: J.P.H. Drenth, The Netherlands
  Speakers panel discussion:
  H. Yazici, Turkey, E. Ben-Chetrit, Israel, P. Hawkins, UK,
D. Kastner, USA, J.W.M. van der Meer, The Netherlands
   
14.30

Plenary session: HIDS + TRAPS + PFAPA

  Chairs: J. Frenkel, The Netherlands & M. Gattorno, Italy
14.30 IgD and immune surveillance
  A. Cerutti, USA
15.00 Adenotonsillectomy in PFAPA as first-line treatment: yes or no?
  M. Hofer, Switzerland
15.30 Analysis of an unfolded protein response and reactive oxygen species generation as a disease mechanism of TRAPS
  J. Dickie, UK
15.45 Reactive Oxygen Species Potentiate LPS-Mediated Inflammation in the TNF Receptor-Associated Periodic
Syndrome (TRAPS)
  A.C.B. Bulua, USA
   
16.00 Discussion
   
16.15 Tea break
   
16.45

Plenary session: Oral presentations HIDS + TRAPS + PFAPA

  Chairs: J. Frenkel, The Netherlands & M. Gattorno, Italy
16.45 TRAPS associated mutations affect a multitude of intracellular pathways beyond the canonical TNFR1 pathways through alterations in both protein abundance and signalling response dynamics.
 

P.J. Tighe, UK

17.00 PFAPA Syndrome – a systems biology approach reveals activation of the innate and adaptive immunity with responsiveness to IL-1ß blockade
 

S. Stojanov, Germany

17.15 TLR2/TLR4-dependent aberrant IL-1 signaling in hyperimmunoglobulinemia D and periodic fever syndrome (HIDS)
 

M. Stoffels, The Netherlands

17.30 Role for Rac1 signaling in the development of autoinflammatory disease
 

R. Van der Burgh, The Netherlands

   

Saturday 4 September 2010

   

08.00

Breakfast Meet-the-Expert session 4

  All about genetics
  I. Touitou, France & J.P.H. Drenth, The Netherlands

Breakfast Meet-the-Expert session 5

  Clinical Phenotype of CAPS
  R. Goldbach-Mansky, USA & H. Hoffman, USA
 

Breakfast Meet-the-Expert session 6

  Basic Science Studying Cytokines
  M. Netea, The Netherlands & C. Dinarello, USA
   

09.00

Plenary session: Regulation of innate immunity

  Chairs: C. Dinarello, USA & M. Netea, The Netherlands
09.00 Dissecting IL-1 and caspase activation
  T. Kanneganti, USA
09.30 Inflammasome activation by dsDNA
  V. Hornung, Germany
10.00 Inflammasome activation
  G. Guarda, Switzerland

10.30

Inflammasome-dependent and -independent activation of IL-1beta

  M. Netea, The Netherlands
   

11.00

Coffee break

   

11.30

Plenary session: Oral presentations Regulation of innate immunity

  Chairs: C. Dinarello, USA & M. Netea, The Netherlands
11.30 Temperature sensitive TRP channels in human peripheral blood mononuclear cells.
  M. Stoffels, The Netherlands
11.45 Endothelial-derived secondary necrotic apoptotic bodies release biologically active IL-1alpha
  P. Kaplanski, France
12.00 Pattern recognition receptors in normal and inflamed human epidermis: upregulation of dectin-1 in psoriasis
  H.D. de Koning, The Netherlands
12.15 Do NALP3 play a role in cytoplasmatic HIV recognition and dendritic cells activation, linking innate to specific immunity in HIV infection?
  A. Pontillo, Italy

 

 

12.30 Lunch
   
12.30 Laptop presentations
   
13.30 Workshop 1
  Basic science issues in the lab: how to measure inflammasome  activation / IL-1 processing?
  Chair: H. Waterham, The Netherlands
Speakers panel discussion: C. Dinarello, USA, M. Netea, The Netherlands, A. Rubartelli, Italy
  Workshop 2
  International Patient Registries
  Chair: J. Frenkel, The Netherlands
Speakers panel discussion: M.Gattorno (Eurofever), Italy, H. Lachmann (Eurotraps), UK, M. Hofer (PFAPA), Switzerland, H. de Koning (Schnitzler), The Netherlands
   
14.30 Plenary session: Autoinflammation versus autoimmunity
  Chair: J.P.H. Drenth, The Netherlands
  Panel members: D. Kastner, D. McGonagle, J. Cohen Tervaert & J. van der Meer
   
16.00

Tea break

   
16.30

Plenary session: CAPS / DIRA / NALP12

  Chairs: R. Goldbach-Mansky, USA & H. Hoffman, USA
16.30 In vivo IL-1 beta regulation in CAPS
  H. Lachmann, UK
17.00 Long-term followup of anakinra in CAPS
  R. Goldbach-Mansky, USA
17.30 Rilonacept in CAPS
  H. Hoffman, USA
   
18.00

Coffee break

   
18.15

Plenary session: Oral presentations CAPS / DIRA / NALP12

  Chairs: R. Goldbach-Mansky, USA & H. Hoffman, USA
18.15 Functional consequences of a germline mutation in the leucin rich repeat domain of NLRP3 identified in an atypical autoinflammatory disorder
 

I. Jéru, France

18.30 Hearing loss in Muckle-Wells-Syndrome – effects of IL-1 inhibition
  J.B. Kuemmerle-Deschner, Germany
18.45

Initial  characterization of a mouse model of neonatal onset multisystem inflammatory disease

  D. Brydges, USA
19.00 A redox signature shared by NLRP3-mutated and NLRP12-mutated monocytes causes accelerated secretion of IL-1ß.
  A. Rubartelli, Italy
   
20.00 Congress dinner

 

 

Sunday 5 September 2010

   

08.30

Workshop 3

  Animal Models for diseases
  Chair: H. Waterham, The Netherlands
  Mouse model FMF
  J. Chae, USA
  Mouse model CAPS
  S. Brydges, USA
  Mouse model HIDS
  H. Waterham, The Netherlands & M. Gibson, USA
  Mouse model CRMO
  P. Ferguson, USA
  Mouse model TRAPS
  R. Siegel, USA
   
 

Workshop 4

  Genetics: quality control and genetic tests
  Chair: I. Touitou, France
  Panel members:
 

I. Aksentijevich, USA

  Y. Shinar, Israel 
 

J. Arostegui, Spain

   

10.00

Coffee break

   

10.30

Plenary session: Other systemic autoinflammatory diseases

  Chairs: J.W.M. van der Meer, The Netherlands & H. Yazici, Turkey
10.30 Treatment of Behcet’s disease
  H. Yazici, Turkey
11.00 The EMBO lecture: Heart failure as a reactive autoinflammatory disease
  C. Dinarello, USA
11.30

Classification of Immunological Disease-Focus on MHC Class 1 intermediate disorders

  D. McGonagle, UK
   
12.00

Plenary session: Oral presentations Other systemic autoinflammatory diseases

  Chairs: J.W.M. van der Meer, The Netherlands & H. Yazici, Turkey
12.00 IL-18 Binding protein (il-18bp) dramatically improves liver histological lesions in an animal model of macrophage activation syndrome (mas).
  P. Kaplanski, France
12.12 PED-BD: An international cohort study on pediatric Behçet’s disease: One-year data of 110 patients
  I. Koné-Paut, France
12.24 Granulomas in NOD2-related Pediatric Granulomatous Arthritis and Crohn’s Disease: an Immunohistochemical Study.
  C.E.I. Janssen
12.36 Mapping dynamic protein interactions of Receptor Interacting Protein 2 (RIP2) and ProCaspase-1 by co-immunoprecipitation and life-cell imaging
  S.R. Hofmann, Germany
12.48 Clinical phenotype and CARD15 gene mutation with Blau Syndrome in Chinese children and their parents
  C.F. Li, China
   
13.00 Lunch
   
13.00 Laptop presentations
   
14.30 Plenary session: Developments in treatment and diagnostics
  Chairs: H. Lachmann, UK & S. Özen, Turkey
14.30 S100A12 protein
  H. Wittkowski, Germany
15.00 Alpha1-antitrypsin
  C. Dinarello, USA
15.30 Developments in IL-1 inhibition
  H. Lachmann, UK
   
16.00 Tea break
   
16.30 Plenary session: Oral presentations Developments in treatment and diagnostics
  Chairs: H. Lachmann, UK & S. Özen, Turkey
16.30 Colchicine does not decrease the need for immunosuppressive use at long term in behçet’s syndrome (bs)
 

G. Hatemi, Turkey

16.42 Safe, Rapid-onset, and Sustained Biological Activity of IL-1ß Regulating Antibody XOMA 052 in Resistant Uveitis of Behçet’s Disease: Preliminary Results of a Pilot Trial
  A. Gul, Turkey
16.54 The role of montelukast in the management of hyperimmunoglobulinemia D with periodic fever
syndrome(HIDS)
  P. Goldsmith, USA
17.06

Experience with anakinra in 120 patients with systemic autoinflammatory diseases

  A. Melo Gomes, Portugal
17.18

On demand rather than continuous anakinra treatment is effective in mevalonate kinase deficiency

  E.J. Bodar, The Netherlands
   
17.30 Plenary session: Oral presentations New Genes and Late Break-through
Chairs: A. Simon, The Netherlands & D. Kastner, USA
17.30

Functional human protein analysis in the post-genome era learning to new autoinflammatory syndrome (Nakajo-Nishimura syndrome)

  H. Ida, Japan
17.45 Identification of the mutation predisposing to a periodic fever syndrome in Chinese Shar-Pei dogs
 

M. Olsson, Sweden

18.00

A novel autoinflammatory syndrome with lymphedema (aisle)

  G. Hatemi, Turkey
18.15

Genome-wide Association Study Identifies Common Variants of the IL10 and IL23R Genes that Contribute to Behçet’s Disease Susceptibility

  F. Remmers, USA
   
Monday 6 September 2010
   

08.00

Breakfast Meet-the-Expert session 7

  Clinical Phenotype of TRAPS
  R. Powell, UK & P. Hawkins, UK
 

Breakfast Meet-the-Expert session 8

  Treatment of FMF
  H. Ozdogan, Turkey & E. Pras, Israel
 

Breakfast Meet-the-Expert session 9

  Clinical Phenotype of PFAPA
  M. Hofer, Switzerland & S. Stojanov, USA
   
09.00 Plenary session: Amyloidosis, other long-term complications and prognosis
  Chairs: B. Hazenberg, The Netherlands & P. Hawkins, UK
09.00 New insights development of AA amyloidosis
  J. van der Hilst, The Netherlands
09.30 Pharmacological depletion of SAP
  P. Hawkins, UK
10.00 Atherosclerosis and the inflammasome in DM type 2
  S. Masters, Ireland
   
10.30 Coffee break
   
11.00 Plenary session: Oral presentations Amyloidosis, other long-term complications and prognosis
  Chairs: B. Hazenberg, The Netherlands & P. Hawkins, UK
11.00

Evaluation of autonomic nervous system dysfunction in FMF patients, with and without amyloidosis

  U. Nussinovitch, Israel
11.15

Causes and predictiors of death and prognosis in familial mediterranean fever in the colchicine era

  G. Can, Turkey
11.30

AA Amyloidosis Complicating the Inherited Periodic Fever Syndromes

  T. Lane, UK
   
11.45 Closing plenary session
  Chairs: J. Frenkel, The Netherlands & J.W.M. van der Meer, The Netherlands
11.45 3 best laptop presentations
12.15  Closing session
  D. Kastner, USA
   
12.45 Closing
  A. Simon, The Netherlands

 

Clinical Challenges for Diagnosis

Establishing the diagnosis of a specific autoinflammatory disease can be very challenging. A few of such diagnostic challenges will be presented to teams of renowned clinicians that will try to solve them during a public discussion on Saturday September 4. You are kindly invited to provide us with complicated cases, where a diagnosis has been reached, or as yet unsolved cases.
Deadline for submission: first of August 2010.

Please contact us (e.erren@ congresscare.com) if you have a suitable case in mind. It is possible to stay anonymous if you prefer, since the aim is purely to examine the diagnostic process in a potential case of autoinflammatory disease.
Friday September 3
13.00 – 14.30

 

Laptop sessions

The usual poster sessions will be substituted by laptop sessions. Instead of bringing a printed-out poster, each laptop presenter will bring his/her own laptop. In the designated area, each presenter will be assigned a standing-table where he or she can talk their audience through their work, using approximately 5 powerpoint slides. The audience will have the opportunity to walk freely between the several laptop presenters. We hope this setup will encourage face-to-face interaction and discussion. For participants who have no laptop, we will provide a small number of laptops on location - please let us know in advance if you need this.
Friday September 3
12.00 – 13.00
Saturday September 4
12.30 – 13.30
Sunday September 5
13.00 – 14.30

 

Meet-the-expert-sessions

These are informal and interactive sessions. The invited experts may prepare a short presentation if they want to, but the main goal of these sessions is to get a chance to ask questions, discuss dilemmas and exchange ideas.
On the on-line registration form, we ask you to choose the sessions you would like to participate in.
Friday September 3
08.00 – 09.00 Meet-the-Expert session 1, 2 & 3
Saturday September 4
08.00 – 09.00 Meet-the-Expert session 4, 5 & 6
Monday September 6
08.00 – 09.00 Meet-the-Expert session 7, 8 & 9